Bilateral clinoidal Rosai Dorfman disease mimicking meningioma – a rare cause of bilateral blindness

Abstract

Rosai Dorfman disease is a self-limiting disease usually affecting the lymph nodes. Intracranial lesions are seen in less than 5% of cases. Isolated intracranial RDD without nodal involvement is rare, only 70 cases have been reported to date. Skull base lesions are seen in only 7 cases, petro clival RDD. Clionoidal lesions of RDD have not been reported in the literature, we report a rare case of bilateral Clionoidal lesions of RDD presenting with bilateral blindness in a young male.