Abstract
Chordoma is a slow-growing malignant bone tumor that develops out of the embryonic notochordal residues and is rare. This is most frequently localized in sacrococcygeal joints, where the localized pain may go unnoticed or be mild in nature, and this may put off a diagnosis. Definitive diagnosis requires the use of histopathology with the assistance of immunohistochemistry. We describe a case of a 45-year-old male with progressive pain and swelling of the gluteal area since few months. Excision biopsy showed lobules of big polygonal physaliphorous cells in a myxoid stroma and had hemorrhage and necrosis. Mitotic activity was low. A chordoma provisional diagnosis was established based on the histomorphology. To prevent recurrence and achieve better outcomes, multidisciplinary management, which consists of surgical excision and long-term follow-up, is necessary.
